CARPEDEM-M3C

Présentation Activités de Recherche M3C-Necker Journées Filière CARDIOGEN 2018

Cardiogen M3C Bonnet 2018 small.pdf

Pour obtenir les informations détaillées concernant les Plans Nationaux de Diagnostic et de Soins (PNDS) en lien avec ls cardiopathies congénitales, connectez vous sur le site de la Haute Autorité de Santé (HAS) https://www.has-sante.fr/portail/jcms/c_1340879/fr/protocoles-nationaux-de-diagnostic-et-de-soins-pnds

PNDS Cardiopathies Congénitales Isolées et Syndromes Associés aux Cardiopathies Congénitales

pnds_transposition des gros vaisseaux.pdf

pnds_fallot et cardiopathies apparentées.pdf

pnds_tonc arteriel commun.pdf

pnds_deletion_22q11_2.pdf

pnds_syndrome_de_williams-beuren.pdf

pnds_rasopathies_syndromes_de_noonan_cardio-facio-cutane_et_apparentes.pdf

pnds_syndrome de turner.pdf

Programme 2018-2019

Cours du Diplôme d'Université de Cardiologie Pédiatrique

Physiologie cardiopathies congénitales simplifiée .pdf

Fallot 2018.pdf

Malpositions Transposition Ventricule droit à double issue Double Discordance 2018.pdf

Cardiomyopathies de l'enfant 2018.pdf

Epidemiologie des Cardiopathies Congénitales.pdf

Génétique des cardiopathies congénitales.pdf

Pathologie coronaire de l'enfant 2018.pdf

Maladie de Kawasaki Actualités 2018*.pdf

Congenital cardiology is a rapidly evolving field involving a complex multidisciplinary approach with a number of complementary medical and surgical strategies. Increasing knowledge is developing in a variety of domains including embryology, molecular genetics, integrative imaging, pharmacotherapy, structural cardiac interventions, electrophysiological optimisation of cardiac function, mechanical circulatory support and heart transplantation. Notwithstanding these technical progress and evolutions, the importance of psycho-social support and care of patients and their families cannot be overstated. The above challenges and dynamics of new developments require guidance for core and advanced medical training in numerous fields of congenital and paediatric cardiology.
The Congenital Cardiology Unit of APHP5 hospital - M3C-Necker is the coordinating site for the “Malformations Cardiaques Congénitales Complexes-M3C” network.
The governance of the M3C is shared with the Congenital Cardiology Unit of Bordeaux, the Adult Congenital Cardiology Unit of the Hôpital Européen Georges Pompidou (part of the Fédération des Cardiopathies Congénitales-APHP, Paris), and the Hôpital Marie Lannelongue (Le Plessis Robinson).
The M3C-Necker is organising on a regular basis a Teaching course and Master Class named “M3C Academy” aiming to develop knowledge and skills in different congenital and paediatric cardiology topics.
This course/master class will take place at the Hôpital Necker Enfants malades twice per year. The agenda of this one and a half day teaching course will be divided into three parts:

1-Master class open to trainees and confirmed paediatric cardiologists, cardiac surgeons and potentially other specialists involved in the care of paediatric cardiac patients or adult congenital patients.
2-Update teaching course on the proposed topic with interactive discussions and analysis of “real-life” cases.
3-Auto-evaluation and post-course evaluation.

Program Master Class & Teaching Course TGA

Thursday November 22nd, 2018
Session 1 10:00 am-01:00 pm – Master Class
How to diagnose foetal transposition of the great arteries? Bertrand Stos, M3C-Necker
Prenatal parents interview: how do I explain TGA and pregnancy issues? Damien Bonnet, M3C-Necker
Management of TGA after delivery: Rashkind procedure, PGE1 infusion, time to surgery, etc. Myriam Bensemlali, M3C-Necker
Arterial switch operation: simple, complex TGA, strategies, information needed, etc. Olivier Raisky, M3C-Necker
Post-operative care: problems and solutions. tba
How do I follow a TGA after an arterial switch? Fanny Bajolle, M3C-Necker

01:00-02:00 pm Lunch

Session 2 02:00 pm – 06:00 pm- Update Teaching course
Hands-on session TGA. Lucile Houyel, M3C Necker
The problem of postoperative evaluation of coronary arteries after the ASO for TGA. Damien Bonnet, M3C Necker
Will we face a big problem with the aortic valve after ASO? Laurence Iserin, M3C-HEGP
How do I follow my patients after an atrial switch for TGA? Laurence Iserin, M3C-HEGP
Neurodevelopmental outcomes in TGA. Leila Kasmi
Quality of life in adult with simple cardiac defects. Pascal Amedro, Montpellier

Friday, November 23rd, 2018
Session 3 08:30 am-11:00 am - Polemics with the M3C staff
I want to terminate pregnancy after my foetus had been diagnosed with a simple TGA.
I do not want my patient to be delivered in the reference center after I had diagnosed a foetal TGA with VSD in a pregnant woman referred to me.
I perform Rashkind procedure in every patient with TGA because I am convinced that it is necessary and also because I need to train myself.
In my institution there is no death after ASO and we have never seen any coronary artery anomaly, therefore we never screen patients for this type of problems.
The only patient of mine who died after ASO developed pulmonary hypertension after two years of age and subsequently died of right heart failure. Probably coincidental association.
The risk of atherosclerotic lesions after the ASO is certainly low as myocardial infarction has not been described in adult patients. I think that it is useless to screen adult patients for myocardial ischemia after ASO for TGA.
I never talk of neurodevelopmental outcomes to parents of a foetus or a child with TGA because they may decide to go for termination or be afraid of mental retardation. My role of physician is also to protect them.

Session 4 11:30 am-12:30 am Evaluation session
Auto-evaluation and post-course evaluation with questionnaire.

12:30 Wrap-up and farewell

Download the booklet with program below

To register use the "contact page"

M3C Academy Teaching course 1 Transposition of the great arteries.pdf